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School of Medicine
Conditions We Treat: Arrhythmogenic Right Ventricular Dysplasia — ARVD (ARVC)
Arrhythmogenic right ventricular dysplasia (ARVD), also known as arrhythmogenic right ventricular cardiomyopathy (ARVC), is a rare but serious inherited disorder that is a common cause of sudden cardiac death in young people. ARVD causes the heart muscle to be replaced by fibrous and fatty tissue, leading to arrhythmias and heart failure.
ARVD (ARVC): What You Need to Know
- Most cases are inherited. If one person is diagnosed with ARVD, then immediate family members (siblings, parents, and children) should be tested for the condition.
- Diagnosis is based on multiple factors from a physical exam, family history, and cardiac tests such as electrocardiogram (ECG/EKG), stress test, Holter monitor, electrophysiology study and cardiac MRI. Cardiac biopsy may be required in rare circumstances.
- The goals of treatment are to prevent sudden cardiac death, improve quality of life by preventing symptomatic cardiac arrhythmias, prevent heart failure and halt progression of the condition.
- People with ARVD should restrict their exercise, which causes progression of the condition and increases the risk of a life-threatening arrhythmia and heart failure.
With proper care that is responsive to each patient's condition over time, ARVD is often successfully managed for decades.
Why choose Johns Hopkins Heart and Vascular Institute for treatment of ARVD?
Our team of cardiologists, electrophysiologists and genetic counselors are committed to improving the lives of people with ARVD.Meet our physicians