Search the Health Library
Get the facts on diseases, conditions, tests and procedures.
I Want To...
Find a Doctor
I Want To...
Find Research Faculty
Enter the last name, specialty or keyword for your search below.
Family Receives the Gift of Hearing
I am so lucky that I live so close,” Tracy says. “I am so thankful for where I am and who I’m dealing with.
The Huegel family was eight hours into a family trip from their home near Baltimore to Michigan when 14-month-old Greta spiked a fever and began grabbing her ears. She was coming down with another ear infection. With no antibiotics to give her daughter, Tracy could only think of one thing to do. Call Dr. Francis at Hopkins.
The Huegels had come to know Howard Francis quite well over the previous eight years. Tracy and Josh both carry a recessive genetic mutation of the Connexin 26 gene, and each of their children were born with a 25 percent chance of being deaf. However, for the Huegels, four of their five children were either born deaf or became deaf at an early age. As the director of the Johns Hopkins Listening Center, Francis performed cochlear implantation surgery on each of the Huegel’s four deaf children.
Tracy was told that someone would find Francis, and ask him for a recommendation. Soon after she hung up, Francis personally returned the call. They coordinated to find a pharmacy that was on the family’s way to Michigan, and he called in a prescription.
“It was really nice to have that connection with him and for him to be a phone call away,” Tracy said. “If there’s an emergency, he’s there to help us.”
The Road to Hopkins
The Huegel’s journey to Johns Hopkins began in 2004 when Tracy became concerned about their first born, Rebecca. She wasn’t responding to her name, could be easily startled, and didn’t react to the noise of her mom vacuuming in her nursery.
By the time she turned 1, Rebecca had been diagnosed as profoundly deaf in both ears. This was the first time Tracy and Josh heard about the cochlear implant. After going to Johns Hopkins for a second opinion, the diagnosis was confirmed. After a lot of research by Josh, the Huegels saw a long track record of innovation and successful patient outcomes and decided Hopkins was the best place for their daughter’s care. At 15-months old, Francis performed Rebecca’s cochlear implantation on her right ear.
After recovering from surgery, patients come back to Hopkins to have their implant activated by an audiologist. As 15-month-old Rebecca sat in her mother’s arms, playing with a box of blocks, the implant was activated. Suddenly, Rebecca stopped playing. She looked up at her mother, touched the implant site, paused, and went back to playing. Rebecca could hear for the first time since she was a newborn.
A Family Affair
After their second child, Jane, was born with no hearing difficulties, the Huegel’s have been regular visitors of The Listening Center as each of their next three children failed their newborn hearing tests and required cochlear implants.
Today, with hearing in both ears, Rebecca is like any other 3rd-grade girl who also happens to be an expert helper at getting her younger siblings to ‘put their ears on’ in the morning.
“I rely on Rebecca,” Tracy says. "If a sitter has questions, (I say) ask Rebecca. They look out for each other.”
As Tracy sits at her kitchen table with five young kids on a stormy summer morning, it is a scene from homes across the country. Kids are laughing and playing, arguing and tattling. Topics range from where the Jolly Ranchers came from to whether the dress-up shoes belong to Rebecca or Jane.
“They argue like every other family,” Tracy says with a smile knowing that this fun, hectic household wouldn’t be the same without cochlear implants.
The Right Choice
As she relives the experiences with each of her kids, Tracy reflects on how lucky she feels that she lives so close to Hopkins.
“They have outstanding doctors that work with you,” she says. “They have a very good connection with their families. Their bedside manner is out of this world. From the time that you go in there, they are very comforting.”
“We take our responsibility of the treatment of these children very seriously,” Francis said. “We recognize that sometimes we’re the only thing that stands between a child being linked into the hearing world and being completely isolated from the hearing world. This is a calling for the team.”
“I am so lucky that I live so close,” Tracy says. “I am so thankful for where I am and who I’m dealing with.”
Learn more abut the treatment team and how they can help you.
The Johns Hopkins Listening Center offers a comprehensive approach to cochlear implantation and is one of the largest cochlear implant programs in the nation. Working with patients of all ages, our staff and faculty are committed to providing a comprehensive network of services to help each of our patients use their cochlear implant to its greatest potential.
For people with severe hearing loss, a cochlear implant may help. Unlike a hearing aid that makes sounds louder, a cochlear implant can help a person with very little or no hearing.