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Conditions We Treat: Arrhythmogenic Right Ventricular Dysplasia — ARVD (ARVC)

Arrhythmogenic right ventricular dysplasia (ARVD), also known as arrhythmogenic right ventricular cardiomyopathy (ARVC), is a rare but serious inherited disorder that is a common cause of sudden cardiac death in young people. ARVD causes the heart muscle to be replaced by fibrous and fatty tissue, leading to arrhythmias and heart failure.

ARVD (ARVC): What You Need to Know

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  • Most cases are inherited. If one person is diagnosed with ARVD, then immediate family members (siblings, parents, and children) should be tested for the condition.
  • Diagnosis is based on multiple factors from a physical exam, family history, and cardiac tests such as electrocardiogram (ECG/EKG), stress test, Holter monitor, electrophysiology study and cardiac MRI. Cardiac biopsy may be required in rare circumstances.
  • The goals of treatment are to prevent sudden cardiac death, improve quality of life by preventing symptomatic cardiac arrhythmias, prevent heart failure and halt progression of the condition.
  • People with ARVD should restrict their exercise, which causes progression of the condition and increases the risk of a life-threatening arrhythmia and heart failure.

With proper care that is responsive to each patient's condition over time, ARVD is often successfully managed for decades.

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Why choose Johns Hopkins Heart and Vascular Institute for treatment of ARVD?

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Our Physicians

Our team of cardiologists, electrophysiologists and genetic counselors are committed to improving the lives of people with ARVD.

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Our Specialty Centers

At the Arrhythmogenic Right Ventricular Dysplasia Center of Excellence, doctors and patients alike are committed to finding a cure for ARVD.

Visit the ARVD Center of Excellence.

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