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Myoclonic Astatic Epilepsy (Doose Syndrome)

What is myoclonic astatic epilepsy (Doose syndrome)? 

Myoclonic astatic epilepsy (MAE), also known as Doose syndrome, is an epilepsy syndrome of early childhood usually characterized by difficult to control generalized seizures. Children will experience drop and staring seizures, sometimes associated with falls.

Symptoms of myoclonic astatic epilepsy (Doose syndrome)

Generally resistant to medication, MAE is a difficult disorder to manage. Patients may experience several seizures daily, and MAE is idiopathic (has no known cause).

Most symptoms of myoclonic astatic epilepsy appear between ages one and five.

Treatment for myoclonic astatic epilepsy (Doose syndrome)

Anticonvulsant medications such as valproate and levetiracetam can be helpful for this condition. However, research in the past decade has shown that the ketogenic diet and modified Atkins diet can be the most effective treatment. 

Request an appointment

For more information about Doose syndrome or to meet with our doctors, request an appointment at the Epilepsy Center.

 

Scheduled for Neurosurgery at Johns Hopkins?

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ONLINE SEMINAR: Epilepsy Surgery: Putting the Puzzle Together

Did you miss the online discussion with neurosurgeon William Anderson on epilepsy surgery? Dr. Anderson discusses treatment option for epilepsy and recent surgical advances that may offer help where medical management and medications have not.

Watch the recording here.

 

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